Health-Related Quality of Life in Patients with the Bladder Exstrophy-Epispadias Complex and Relationship to Incontinence and Sexual Factors: A Review of the Recent Literature

Gundela Holmdahl; Michaela Dellenmark-Blom; Agneta Nordenskjöld; Sofia Sjöström

doi:10.1055/s-0040-1713178

European Journal of Pediatric Surgery, Inhaltsverzeichnis

Eur J Pediatr Surg 2020; 30(03): 251-260
DOI: 10.1055/s-0040-1713178

Review Article

Georg Thieme Verlag KG Stuttgart · New York

Health-Related Quality of Life in Patients with the Bladder Exstrophy-Epispadias Complex and Relationship to Incontinence and Sexual Factors: A Review of the Recent Literature

Gundela Holmdahl

¹Department of Pediatric Surgery, Karolinska University Hospital, Astrid Lindgren Children’s Hospital, Stockholm, Sweden

²Department of Pediatric Surgery, Pediatric Uronephrologic Center at the Queen Silvia Childrens Hospital, Institution of Clinical Sciences, Sahlgrenskas University Hospital, Gothenburg Sweden

,

Michaela Dellenmark-Blom

²Department of Pediatric Surgery, Pediatric Uronephrologic Center at the Queen Silvia Childrens Hospital, Institution of Clinical Sciences, Sahlgrenskas University Hospital, Gothenburg Sweden

,

Agneta Nordenskjöld

¹Department of Pediatric Surgery, Karolinska University Hospital, Astrid Lindgren Children’s Hospital, Stockholm, Sweden

³Department of Women’s and Children’s Health and Center for Molecular Medicine, Karolinska Institute, Stockholm, Sweden

,

Sofia Sjöström

²Department of Pediatric Surgery, Pediatric Uronephrologic Center at the Queen Silvia Childrens Hospital, Institution of Clinical Sciences, Sahlgrenskas University Hospital, Gothenburg Sweden

› Institutsangaben

Abstract

The bladder exstrophy-epispadia complex (BEEC) includes malformations with midline closing defects of the lower abdomen and external genitalia. Long-term consequences with urinary incontinence and sexual dysfunction, in spite of multiple surgical interventions, are common and expected to affect the patient's health-related quality of life (HRQOL). The extent and the predictive factors are, however, not known. New patient-reported outcome research is emerging, but valid and reliable condition-specific HRQOL are still missing. The aim of this review is to summarize and discuss the latest published reports (2015–2019) on HRQOL in patients with the BEEC and its relationship to incontinence and sexual factors.

Keywords

bladder exstrophy - epispadias - health-related quality of life - incontinence - sexual factors

Volltext

Referenzen

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